Guillain-Barré 증후군 양상으로 발병한 원발성 척추내 말초성 원시신경외배엽종양 1례

• 영문명: A Case of Primary Intraspinal Peripheral Primitive Neuroectodermal Tumor (pPNET) Mimicking Guillain-Barré Syndrome
• 발행기관: 대한소아신경학회
• 저자명: 이정용(Jeong Yong Lee) 이은혜(Eun Hye Lee) 정민희(Min Hee Jeong) 염미선(Mi-Sun Yum) 임호준(Ho Joon Im) 서종진(Jong Jin Seo) 나영신(Young-Shin Ra) 고태성(Tae-Sung Ko)
• 간행물 정보: 『Annals of Child Neurology(구 대한소아신경학회지)』대한소아신경학회지 제18권 제2호, 326~331쪽, 전체 6쪽
• 주제분류: 의약학 > 소아과학
• 파일형태: PDF
• 발행일자: 2010.11.30

영문 초록

Primary intraspinal peripheral primitive neuroectodermal tumors (pPNET) are ex- tremely rare. We report a 10-month-old girl presented with rapidly progressive pa- raparesis and raised cerebrospinal fluid protein. A magnetic resonance image demon- strated an intramedullary mass from C3 to T3 level and intradural extramedullary nodules in the lumbosacral area. Surgery was performed with partial tumor removal and histologic examination revealed a small round cell tumor and immunohistoche- mical characteristics of pPNET. She died due to tumor progression at four months after initial diagnosis. This case has been reported to raise awareness among clini- cians to include the possibility of intraspinal tumors in the differential diagnosis of progressive neurological deficits mimicking Guillain-Barré syndrome.

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키워드

Guillain-Barré Syndrome Neuroectodermal Tumors Primitive Peripheral