Endoscopic transnasal anterior clinoidectomy for optic canal unroofing in a patient with fibrous dysplasia of the sphenoid bone

• 발행기관: 대한두개저학회
• 저자명: Juan Luis Gó mez-Amador Marcos Vinicius Sangrador-Deitos Luis Alberto Rodriguez Hernandez Aldo Gabriel Eguiluz Melé ndez
• 간행물 정보: 『대한두개저학회지』제16권 제2호, 114~119쪽, 전체 6쪽
• 주제분류: 의약학 > 일반외과학
• 파일형태: PDF
• 발행일자: 2021.09.30

영문 초록

Fibrous dysplasia (FD) is a rare, benign disease, characterized by the replacement of normal medullary bone by fibro-osseous tissue. It is caused by somatic mutations in the α subunits of the stimulatory G protein encoded by the GNAS gene. FD can be divided into three categories. FD must be considered with any clival, sellar or parasellar lesion, especially with bone affection. Visual disturbances are one of the most disabling complications of this disease, secondary to optic canal compression. There is still controversy whether unroofing of the optic canal should be performed in these cases. We present the case of a 30-year-old woman who presented to our institution with a 3 weeks history of headache and blurred vision, for which a neuronavigated transnasal endoscopic resection was planned. We present a novel surgical approach, in which we performed a conventional transellar approach, with complete resection of an osseous lesion which infiltrated the sella turcica and clivus. Unroofing of the left optic canal and complete decompression of the optic nerve were performed, as well as an extradural clinoidectomy.

목차

INTRODUCTION

CASE REPORT

DISCUSSION

키워드

Anterior clinoid Clivus Monostotic fibrous dysplasia Neuroendoscopy