앞허혈시신경병증으로 발견된 모야모야병 1예

• 영문명: A Case of Moyamoya Disease Initially Presenting as Anterior Ischemic Optic Neuropathy
• 발행기관: 대한안과학회
• 저자명: 조아란 김소영,Aran Cho, MD, So Young Kim, MD, PhD,
• 간행물 정보: 『대한안과학회지』Ophthalmological Society,volume52,number7, 887~892쪽, 전체 6쪽
• 주제분류: 의약학 > 기타의약학
• 파일형태: PDF
• 발행일자: 2011.07.15

영문 초록

Purpose: To present a case of a patient with decreased visual acuity and anterior ischemic optic neuropathy diagnosed with advanced Moyamoya disease. Case summary: A 46-year-old woman presented sudden episodes of headache and decreased visual acuity. On her first visit, her best corrected visual acuity was 20/25 in the right eye and 20/70 in the left eye. The left eye pupil was dilated with a relative afferent papillary defect. Fundus examinations revealed disc swelling in the left eye. After being admitted, steroid pulse therapy was started and Magnetic Resonance Imaging (MRI) studies revealed Moyamoya disease. The diagnosis was confirmed via Magnetic Resonance Angiography (MRA). After steroid pulse therapy, the headaches and visual acuity improved and the patient is continuing follow-up visits at neurosurgery and ophthalmology clinics. Conclusions: Patients with Moyamoya disease may initially present symptoms and signs of anterior ischemic optic neuropathy. J Korean Ophthalmol Soc 2011;52(7):887-892

키워드

Moyamoya disease, Optic neuropathy, Steroid pulse therapy