Von Hippel-Lindau 증후군 환자에서 발생한 비강내 혈관종

• 영문명: A Case of Hemangioma of Nasal Cavity in Von Hippel-Lindau Syndrome
• 발행기관: 대한두경부종양학회
• 저자명: 강현석 정수진 채승완 홍석진
• 간행물 정보: 『대한두경부종양학회지』제39권 제2호, 65~69쪽, 전체 5쪽
• 주제분류: 의약학 > 종양학
• 파일형태: PDF
• 발행일자: 2023.11.30

국문 초록

We report a unique case of hemangioma of the nasal cavity in von Hippel-Lindau (VHL) syndrome. A 26-yearold female with VHL syndrome who had previously undergone surgery for pancreatic and adrenal mass presented with a 4-month history of left-sided nasal obstruction. The patient had an expansile mass lesion in the left nasal cavity and an imaging test demonstrated the mass in the left maxillary sinus extending to the nasal cavity. The tumor was removed with an endoscopic prelacrimal recess approach considering the possibility of not only a benign tumor such as hemangioma but also a malignant tumor of the maxillary sinus and histopathologic examination confirmed cavernous hemangioma. This case is the rarely reported manifestation of the paranasal sinus in VHL disease.

키워드

Endoscopy Hemangioma Maxillary sinus neoplasms von Hippel Lindau disease