구강과 측인두강 및 전신에 발생한 신경섬유종증

• 영문명: MULTIPLE NEUROFIBROMATOSIS WITH ORAL, PARAPHARYNGEAL SPACE AND WHOLE BODY LESIONS
• 발행기관: 대한구강악안면외과학회
• 저자명: 오송섭(Seong Seob Oh) 황홍준(Hong Jun Hwang) 김일규(Il Kyu Kim) 최진호(Jin Ho Cho) 김형돈(Hyung Don Kim) 오남식(Nam Sik Oh) 박은진(Eun Jin Park)
• 간행물 정보: 『대한구강악안면외과학회지』대한구강악안면외과학회지 제25권 제2호, 178~181쪽, 전체 4쪽
• 주제분류: 의약학 > 내과학
• 파일형태: PDF
• 발행일자: 1999.04.30

영문 초록

Neurofibromatosis(Von Recklinghausen s disease) is an autosomal dominant disease that affects one in 2,500-3,000 births. The clinical presentation is characterized by multiple pigmented lesions of the skin, known as cafe-au-lait spots, and neurofibromas of the skin. The criteria for diagnosis are at least six cafe-au-lait spots, each greater than 1.5㎝ in diameter and positive family history and biopsy of a neurofibroma. Management of benign neurofibromatosis must be individualized for each patient and ranges from incisional biopsy to wide local excision. Genetic counseling is advised for all patients with this disease, since no cure is available. We report the case of multiple neurofibromatosis with oral, parapharyngeal space and whole body lesions that was treated with surgical excision.

목차

Abstract

Ⅰ. 서론

Ⅱ. 증례보고

Ⅲ. 총괄 및 고찰

Ⅳ. 결론

참고문헌