기저세포모반증후군과 관련된 악골의 다발성 치성각화낭종의 치험례

• 영문명: A CASE REPORT OF MULTIPLE ODONTOGENIC KERATOCYSTS ASSOCIATED WITH BASAL CELL NEVUS SYNDROME
• 발행기관: 대한구강악안면외과학회
• 저자명: 변준호(June Ho Byun) 박성희(Seong Hee Park) 김욱규(Uc Kyu Kim) 박혜련(Hae Ryoun Park) 정인교(In Kyo Chung)
• 간행물 정보: 『대한구강악안면외과학회지』대한구강악안면외과학회지 제26권 제3호, 305~309쪽, 전체 5쪽
• 주제분류: 의약학 > 내과학
• 파일형태: PDF
• 발행일자: 2000.06.30

영문 초록

The basal cell nevus syndrome is a well recognized entity, the major symptoms of which are basal cell nevi, multiple jaw cysts, skeletal anomalies, and ectopic calcification. The syndrome follows a hereditary pattern, which is characterized by a highly penetrant, autosomal dominant gene with multiple and variable effects. The patient often has a characteristic face, with frontal and temporoparietal bossing, which results in an increased cranial circumference. The eyes may appear widely separated, and 40 percent of patients have true ocular hypertelorism. Jaw cysts are one of the most constant features of the syndrome and are present in at least 75 percent of the patients. The cysts are odontogenic keratocysts and frequently multiple. Radiographically, the cysts in patients with basal cell nevus syndrome do not differ significantly from isolated keratocysts. The cysts in patients with this syndrome are often associated with the crowns of unerupted teeth; on radiographs they may mimic dentigerous cysts. We report a case of multiple odontogenic keratocysts associated with basal cell nevus syndrome with the literature of review.

목차

Abstract

Ⅰ. 서론

Ⅱ. 증례보고

Ⅲ. 총괄 및 고찰

Ⅳ. 결론

참고문헌

키워드

Basal cell nevus syndrome Multiple odontogenic keratocysts